Search on: GRANULOMATOSIS WITH POLYANGIITIS 
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Descriptor English:   Granulomatosis with Polyangiitis 
Descriptor Spanish:   granulomatosis con poliangitis 
Descriptor Portuguese:   Granulomatose com Poliangiite 
Synonyms English:   Granulomatosis with Polyangiitides
Granulomatosis, Wegener
Granulomatosis, Wegener's
Polyangiitides, Granulomatosis with
Polyangiitis, Granulomatosis with
Wegener Granulomatosis
Wegener's Granulomatosis
with Polyangiitides, Granulomatosis
with Polyangiitis, Granulomatosis  
Tree Number:   C08.381.483.950
C14.907.940.897.249.750
C20.111.193.875
Definition English:   A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN. 
See Related English:   Myeloblastin
Vasculitis, Central Nervous System
 
History Note English:   2015(1963) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   27929 
Unique Identifier:   D014890 

Occurrence in VHL:
 

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